Intractable Rare Dis Res. 2017;6(2):150-151. (DOI: 10.5582/irdr.2017.01008)

Pancreatic lipomatosis in cystic fibrosis: Rare manifestation of an uncommon disease.

Mandavdhare HS, Kumar A, Sharma V, Rana SS


Cystic fibrosis is deemed to be uncommon in India. The presentation is usually in the childhood although more cases are now being recognized in adolescence and adulthood. We report a case of an adolescent male who had been treated for recurrent pulmonary infections and received anti-tubercular therapy for a possible diagnosis of sputum negative pulmonary tuberculosis and was evaluated for steatorrhea. The presence of pancreatic exocrine insufficiency along with pancreatic lipomatosis suggested the diagnosis of cystic fibrosis.

KEYWORDS: Cystic fibrosis, bronchiectasis, pancreatic exocrine insufficiency, steatorrhea, endoscopic ultrasound

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