Intractable Rare Dis Res. 2015;4(4):203-206. (DOI: 10.5582/irdr.2015.01025)

An isolated single L-II type coronary artery anomaly: A rare coronary anomaly.

Ermis E, Demirelli S, Korkmaz AF, Dilekci Sahin B, Kantarci A


The incidence of congenital artery anomalies is 0.2-1.4%, and most are benign. Single coronary artery (SCA) anomalies are very rare. The right coronary artery (RCA) originating from the left coronary system is one such SCA anomaly, and the risk of sudden cardiac death (SCD) increases if it courses between the pulmonary artery and aorta and coexists with other congenital heart diseases. Additionally, coursing of the RCA between the great vessels increases the risk of atherosclerosis. We herein present the case of a 57 year-old man who was admitted to our cardiology outpatient clinic and diagnosed with an SCA anomaly in which the RCA arose from the left main coronary artery (LMCA) and coursed between the pulmonary artery and aorta. However a critical stenosis was not detected in imaging techniques, and myocardial perfusion scintigraphic evidence of ischaemia was found in a small area. Therefore, he was managed with conservative medical therapy.

KEYWORDS: Coronary vessel anomalies, coronary angiography, multidetector computed tomography

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